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Texas Creutzfeldt-Jakob Disease Case Counts by Type of Disease and Year (2009-2018) |
Classifi- cation
|
Trans- mission Type
|
Disease Type
|
2009
|
2010
|
2011
|
2012
|
2013
|
2014
|
2015
|
2016
|
2017
|
2018
|
Total Counts
|
Confirmed
|
Acquired
|
vCJD
|
|
|
|
|
|
1 |
|
|
|
|
1 |
Familial
|
fCJD
|
2 |
2 |
|
|
|
3 |
|
|
1 |
2 |
10 |
FFI
|
|
2 |
|
|
|
|
|
|
|
|
2 |
Sporadic |
sCJD
|
10 |
16 |
12 |
10 |
10 |
11 |
14 |
18 |
15 |
21 |
137 |
sFI
|
|
|
1 |
|
|
|
|
|
|
1 |
2 |
VPSPr
|
|
|
|
1 |
|
1 |
|
|
1 |
|
3 |
Probable
|
Familial
|
fCJD
|
|
|
|
1 |
|
1 |
1 |
1 |
|
|
4 |
Sporadic
|
sCJD
|
6 |
8 |
5 |
10 |
4 |
10 |
4 |
14 |
8 |
11 |
80 |
Possible |
Sporadic
|
sCJD
|
2 |
|
|
|
|
|
1 |
|
|
1 |
4 |
Total Counts
|
20
|
28
|
18
|
22
|
14
|
27
|
20
|
33
|
25
|
36
|
243
|
vCJD: variant Creutzfeldt-Jakob Disease; fCJD: familial Creutzfeldt-Jakob Disease; FFI: Fatal Familial Insomnia; sCJD: sporadic Creutzfeldt-Jakob Disease; sFI: sporadic Fatal Insomnia; VPSP: variably protease-sensitive prionopathy |
Texas Creutzfeldt-Jakob Disease Deaths and Death Rates per Year (2009-2018)
|
Case Year
|
Case Counts
|
Case Rate per Million Population
|
2009
|
20 |
0.81 |
2010
|
28 |
1.11 |
2011
|
18 |
0.7 |
2012
|
22 |
0.84 |
2013
|
14 |
0.53 |
2014
|
27 |
0.99 |
2015
|
20 |
0.72 |
2016
|
33 |
1.17 |
2017
|
25 |
0.87 |
2018
|
36 |
1.22 |
Average
|
24.3 |
0.9 |
Average Number of Texas Cases per Year = 24.3
Average Rate of Deaths/Million Population/10 years = 0.9 |

Creutzfeldt-Jakob Disease Case Counts by Gender and Year (2009-2018) |
Gender
|
2009
|
2010
|
2011
|
2012
|
2013
|
2014
|
2015
|
2016
|
2017
|
2018
|
Totals
|
Male
|
8 |
12 |
10 |
12 |
6 |
11 |
9 |
18 |
9 |
14 |
109
|
Female
|
12 |
16 |
8 |
10 |
8 |
16 |
11 |
15 |
16 |
22 |
134
|
Total Counts
|
20
|
28
|
18
|
22
|
14
|
27
|
20
|
33
|
25
|
36 |
243
|
|
Gender
|
2009
|
2010
|
2011
|
2012
|
2013
|
2014 |
2015
|
2016
|
2017
|
2018
|
Avg %
|
% Males
|
40% |
43% |
56% |
55% |
43% |
41% |
45% |
55% |
36% |
39% |
45%
|
% Females
|
60% |
57% |
44% |
45% |
57% |
59% |
55% |
45% |
64% |
61% |
55%
|